0
Case Reports   |    
Severe Myelopathy Resulting from Melorheostosis of the Cervicothoracic SpineA Case Report
Steven C. Zeiller, MD1; Alexander R. Vaccaro, MD2; David W. Wimberley, MD1; Todd J. Albert, MD2; James S. Harrop, MD3; Alan S. Hilibrand, MD2
1 Department of Orthopaedic Surgery, Thomas Jefferson University, 1015 Chestnut Street, Philadelphia, PA 19107. E-mail address for S.C. Zeiller: zeiller@comcast.net
2 Thomas Jefferson University, Rothman Institute, 925 Chestnut Street, Philadelphia, PA 19107
3 Department of Neurosurgery, Jefferson Medical College, 909 Walnut Street, Second Floor, Philadelphia, PA 19107
View Disclosures and Other Information
The authors did not receive grants or outside funding in support of their research or preparation of this manuscript. They did not receive payments or other benefits or a commitment or agreement to provide such benefits from a commercial entity. No commercial entity paid or directed, or agreed to pay or direct, any benefits to any research fund, foundation, educational institution, or other charitable or nonprofit organization with which the authors are affiliated or associated.
Investigation performed at the Department of Orthopaedic Surgery, Thomas Jefferson University, Philadelphia, Pennsylvania

The Journal of Bone and Joint Surgery, Incorporated
J Bone Joint Surg Am, 2005 Dec 01;87(12):2759-2762. doi: 10.2106/JBJS.D.02653
5 Recommendations (Recommend) | 3 Comments | Saved by 3 Users Save Case

Extract

Melorheostosis is a rare, noninheritable, benign sclerosing bone dysplasia. The condition was originally described in 1922 by Leri and Joanny1. The disease process is of mesodermal origin, and the minimum prevalence is believed to be 0.9 cases per million2. Melorheostosis typically affects the long bones of the skeleton with the lower extremities being more commonly involved. In addition, the bones of the hand and foot may be involved with the disease process. Involvement of the axial skeleton, especially in Garver isolation, is very rare3. We describe a unique case of a patient who had severe spinal stenosis of the lower cervical and upper thoracic spine due to melorheostosis, resulting in progressive myelopathy. Our patient was notified that data concerning the case would be submitted for publication.
Figures in this Article

    First Page Preview

    View Large
    />
    First page PDF preview
    Sign In to Your Personal ProfileSign In To Access Full Content
    Not a Subscriber?
    Get online access for 30 days for $35
    New to JBJS?
    Sign up for a full subscription to both the print and online editions
    Register for a FREE limited account to get full access to all CME activities, to comment on public articles, or to sign up for alerts.
    Register for a FREE limited account to get full access to all CME activities
    Have a subscription to the print edition?
    Current subscribers to The Journal of Bone & Joint Surgery in either the print or quarterly DVD formats receive free online access to JBJS.org.
    Forgot your password?
    Enter your username and email address. We'll send you a reminder to the email address on record.

     
    Forgot your username or need assistance? Please contact customer service at subs@jbjs.org. If your access is provided
    by your institution, please contact you librarian or administrator for username and password information. Institutional
    administrators, to reset your institution's master username or password, please contact subs@jbjs.org

    References

    Accreditation Statement
    These activities have been planned and implemented in accordance with the Essential Areas and policies of the Accreditation Council for Continuing Medical Education (ACCME) through the joint sponsorship of the American Academy of Orthopaedic Surgeons and The Journal of Bone and Joint Surgery, Inc. The American Academy of Orthopaedic Surgeons is accredited by the ACCME to provide continuing medical education for physicians.
    CME Activities Associated with This Article
    Submit a Comment
    Please read the other comments before you post yours. Contributors must reveal any conflict of interest.
    Comments are moderated and will appear on the site at the discretion of JBJS editorial staff.

    * = Required Field
    (if multiple authors, separate names by comma)
    Example: John Doe





    Related Content
    The Journal of Bone & Joint Surgery
    JBJS Case Connector
    Topic Collections
    Related Audio and Videos
    Clinical Trials
    Readers of This Also Read...
    JBJS Jobs
    12/31/2013
    S. Carolina - Department of Orthopaedic Surgery Medical Univerity of South Carlonina
    04/02/2014
    W. Virginia - Charleston Area Medical Center
    12/04/2013
    New York - Icahn School of Medicine at Mount Sinai
    02/28/2014
    District of Columbia (DC) - Children's National Medical Center