Melorheostosis is a rare, noninheritable, benign sclerosing bone dysplasia.
The condition was originally described in 1922 by Leri and
Joanny1. The disease
process is of mesodermal origin, and the minimum prevalence is believed to be
0.9 cases per
Melorheostosis typically affects the long bones of the skeleton with the lower
extremities being more commonly involved. In addition, the bones of the hand
and foot may be involved with the disease process. Involvement of the axial
skeleton, especially in Garver isolation, is very
rare3. We describe a
unique case of a patient who had severe spinal stenosis of the lower cervical
and upper thoracic spine due to melorheostosis, resulting in progressive
myelopathy. Our patient was notified that data concerning the case would be
submitted for publication.