RT Journal
A1 Crawford, Eileen A.
A1 Brooks, John S.J.
A1 Ogilvie, Christian M.
T1 Osteosarcoma of the Proximal Part of the Radius in Mazabraud SyndromeA Case Report
JF The Journal of Bone & Joint Surgery
JO The Journal of Bone & Joint Surgery
YR 2009
FD April 1
VO 91
IS 4
SP 955
OP 960
DO 10.2106/JBJS.H.00212
UL http://dx.doi.org/10.2106/JBJS.H.00212
AB 
Malignant transformation of fibrous dysplasia into sarcoma is a rare event, occurring in less than 1% of cases1,2. Malignant transformation of fibrous dysplasia can also occur as part of Mazabraud syndrome, a syndrome characterized by fibrous dysplasia and intramuscular myxomas1. However, Mazabraud syndrome is so rare that only four cases of sarcomatous degeneration have been reported in the literature1,3-5. Here we report a fifth case, which involved the development of osteosarcoma in a fibrous dysplastic lesion of the proximal part of the radius in a patient with Mazabraud syndrome.