TY  - JOUR
T1  - Successful Elbow Contracture Release Secondary to MelorheostosisA Case Report
AU  - Gong, Hyun Sik
AU  - Lee, Kyung Hak
AU  - Oh, Joo Han
AU  - Chung, Jin-Haeng
AU  - Baek, Goo Hyun
AU  - Chung, Moon Sang
Y1  - 2008/05/01
N1  - 10.2106/JBJS.G.00961
JO  - The Journal of Bone & Joint Surgery
SP  - 1106
EP  - 1111
VL  - 90
IS  - 5
N2  - 
Melorheostosis is a rare, noninheritable developmental dysplasia of cortical bone that is often characterized by a classic radiographic pattern of flowing hyperostosis along the cortex of long bones1. Patients with this condition may have joint pain, stiffness, deformity, and restricted range of motion due to soft-tissue contracture2. Involvement usually follows a sclerotomal distribution3 and usually affects only one extremity4,5. Joint contracture occurs when the abnormal ossification in the cortex of the long bone involves the soft tissues and extends into the joint, resulting in soft-tissue fibrosis and contracture2,5,6. There is no specific treatment for this condition; options range from nonsurgical management (e.g., splinting and early training in making optimal use of the unaffected extremity) to various types of surgical management (e.g., tendon lengthening, sympathectomy, implant arthroplasty, or even amputation2. The literature indicates that surgical release of a joint contracture may be difficult and that recurrence of the deformity is frequent2,4-6.

SN  - 0021-9355
M3  - doi: 10.2106/JBJS.G.00961
UR  - http://dx.doi.org/10.2106/JBJS.G.00961
ER  -