TY - JOUR T1 - Familial Dystopic Os OdontoideumA Report of Three Cases AU - Wang, Shenglin AU - Wang, Chao Y1 - 2011/05/04 N1 - 10.2106/JBJS.J.01018 JO - The Journal of Bone & Joint Surgery SP - e44 1 EP - 5 VL - 93 IS - 9 N2 - In 1886, Giacomini1 described a rare lesion of the axis, os odontoideum, which was defined as an ossicle, consisting of smooth and separate caudal portions of the odontoid process. When it occurs, the caudal fragment of the odontoid may provide deficient stability for the atlantoaxial joint and lead to subsequent instability or dislocation and neurological deficits2-4. According to its location, os odontoideum has been classified into two anatomic types: orthotopic and dystopic4. Orthotopic os odontoideum consists of an ossicle that moves with the anterior arch of the atlas, while the dystopic type consists of an ossicle near the basion, or one that is fused with the clivus4. SN - 0021-9355 M3 - doi: 10.2106/JBJS.J.01018 UR - http://dx.doi.org/10.2106/JBJS.J.01018 ER -